Abstract
Approximately 85-90% of all rhabdomyosarcoma (RMS) cases occur in children and adolescents. In adults, RMS accounts for only 2-5% of all soft tissue sarcomas. The annual incidence in adults is 0.3-0.5 per 1,000,000 and is classified as a “very rare tumor.” More than 95% of RMSs are extragastric. Primary gastric RMS is reported extremely rarely in adults, and the estimated incidence is <0.01/1,000,000/year. This rate is <0.01% of all gastric malignancies and <1% of all adult RMSs. We report the 18F-fluorodeoxyglucose positron emission tomography/computed tomography findings in an adult with primary gastric alveolar RMS, highlighting the metabolic characteristics of this extraordinarily rare malignancy.
Keywords:
Rhabdomyosarcoma, alveolar rhabdomyosarcoma, 18F-FDG PET/CT, primary gastric rhabdomyosarcoma, rare malignancy
Ethics
Informed Consent: Written informed consent was obtained from the patient for the 18F-FDG PET/CT examination.
Authorship Contributions
Surgical and Medical Practices: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Consept: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Design: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Data Collection or Processing: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Analysis or Interpretation: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Literature Search: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A., Writing: B.Y.B., İ.B., C.L., İ.T.R., E.A., G.A., E.A.
Conflict of Interest: No conflicts of interest were declared by the authors.
Financial Disclosure: The authors declare that this study has received no financial support.
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